Osteogenesis imperfecta

In addition to dentinogenesis imperfecta, other dental alterations can be observed in OI. Some of these alterations can only be detected through dental X-rays.

Teeth in OI can be of normal size, but in some patients, they may be smaller with shorter roots. X-rays often reveal crowns with a bulbous appearance and wider or obliterated pulp chambers: where the pulp is located, dentin occupies the space of the pulp.

Other dental alterations observed in OI include:

• Dental agenesis: the absence of one or several teeth (teeth that do not erupt and are not visible on X-rays).
• Supernumerary teeth: the presence of one or more extra teeth, exceeding the usual number of teeth (more than 20 primary teeth or more than 32 permanent teeth).
• Ectopic eruption: teeth that emerge outside their correct alignment in the dental arch.
• Accelerated eruption: accelerated tooth replacement and early eruption of permanent dentition.
• Dental impaction: teeth that fail to erupt and remain impacted in the bone or gum tissue (but can be identified on X-rays).